Successful Prenatal Treatment of Cardiac Rhabdomyoma in a Fetus with Tuberous Sclerosis
Abstract
:1. Introduction
2. Case Description
3. Discussion
4. Conclusions
Supplementary Materials
Author Contributions
Funding
Institutional Review Board Statement
Informed Consent Statement
Data Availability Statement
Acknowledgments
Conflicts of Interest
References
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Parameter | Unit | GA 27 Weeks | GA 31 Weeks | GA 37 Weeks | GA 39 Weeks * | Reference Values |
---|---|---|---|---|---|---|
CD4 cells | /nL | 0.92 | 0.96 | 0.97 | 0.50–1.20 | |
CD8 cells | /nL | 0.33 | 0.38 | 0.37 | 0.30–0.80 | |
CD4/CD8 | ratio | 2.8 | 2.5 | 2.6 | 1.1–3.0 | |
NK cells | /nL | 0.05 | 0.10–0.40 | |||
Hemoglobin | g/dL | 11.8 | 11.3 | 11.1 | 10.2 | 12.0–15.6 |
Erythrocytes | /pL | 3.7 | 3.5 | 3.7 | 3.4 | 3.9–5.2 |
Leukocytes | /nL | 8.89 | 7.38 | 7.76 | 7.96 | 3.90–10.50 |
Thrombocytes | /nL | 178 | 209 | 193 | 189 | 150–370 |
Creatinin | mg/dL | 0.66 | 0.59 | 0.50–0.90 | ||
GPT (ALT) | U/L | 9 | 15 | 20 | <31 | |
GOT (AST) | U/L | 16 | 24 | 26 | <35 | |
Cholesterin | mg/dL | 250 | 294 | 301 | <200 | |
LDL-Cholesterin | mg/dL | 163 | 200 | 193 | <130 | |
Triglycerides | mg/dL | 174 | 256 | 351 | <200 | |
CMV-DNA | copies/mL | 0 | 0 | 0 | ||
EBV-DNA | copies/mL | 0 | 0 | |||
Sirolimus | ng/mL | 8.91 | 8.40 | 1.16 ** |
Parameter | Unit | Postnatal Day 1 | Postnatal Day 3 | Postnatal Day 5 | Reference Values |
---|---|---|---|---|---|
CD4 cells | /nL | 1.66 | 1.96 | 0.40–3.50 | |
CD8 cells | /nL | 0.57 | 0.66 | 0.20–1.90 | |
CD4/CD8 | ratio | 2.9 | 3.0 | 1.0–2.6 | |
NK cells | /nL | 0.05 | 0.12 | 0.10–1.90 | |
CRP | mg/L | <0.6 | <5.0 | ||
IL 6 | ng/L | 2.2 | <66.4 | ||
Hemoglobin | g/dL | 18.2 | 19.0 | 13.2–21.7 | |
Erythrocytes | /pL | 4.8 | 5.3 | 3.9–6.3 | |
Leukocytes | /nL | 14.55 | 6.95 | 9.00–28.20 ** 7.20–21.60 *** | |
Thrombocytes | /nL | 238 | 2.52 | 220–520 | |
Sirolimus | ng/mL | 1.59 * |
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Will, J.C.; Siedentopf, N.; Schmid, O.; Gruber, T.M.; Henrich, W.; Hertzberg, C.; Weschke, B. Successful Prenatal Treatment of Cardiac Rhabdomyoma in a Fetus with Tuberous Sclerosis. Pediatr. Rep. 2023, 15, 245-253. https://doi.org/10.3390/pediatric15010020
Will JC, Siedentopf N, Schmid O, Gruber TM, Henrich W, Hertzberg C, Weschke B. Successful Prenatal Treatment of Cardiac Rhabdomyoma in a Fetus with Tuberous Sclerosis. Pediatric Reports. 2023; 15(1):245-253. https://doi.org/10.3390/pediatric15010020
Chicago/Turabian StyleWill, Joachim Carsten, Nina Siedentopf, Oliver Schmid, Teresa Mira Gruber, Wolfgang Henrich, Christoph Hertzberg, and Bernhard Weschke. 2023. "Successful Prenatal Treatment of Cardiac Rhabdomyoma in a Fetus with Tuberous Sclerosis" Pediatric Reports 15, no. 1: 245-253. https://doi.org/10.3390/pediatric15010020
APA StyleWill, J. C., Siedentopf, N., Schmid, O., Gruber, T. M., Henrich, W., Hertzberg, C., & Weschke, B. (2023). Successful Prenatal Treatment of Cardiac Rhabdomyoma in a Fetus with Tuberous Sclerosis. Pediatric Reports, 15(1), 245-253. https://doi.org/10.3390/pediatric15010020